Skull Base & Neuro-Ophthalmology Surgical Neurology International (2021) 2 Scholar Citations

Ectopic intraconal orbital meningioma–A rare case report

Authors: A. K. Sharma, C. S. Gandhoke, S. Misra, A. Ravi, R. K. Gupta, Dr. Surendra K. Gupta

Published in: Surgical Neurology International | Volume 12, Article 305

Key Clinical Findings & Highlights

  • Details lateral micro-orbitotomy technique for retrobulbar tumors.
  • Achieves 100% vision preservation with complete proptosis reversal.
  • Highlights histological confirmation of ectopic arachnoid cell origin.

Abstract

Primary intraorbital meningiomas that arise entirely within the retrobulbar intraconal space without attachment to the optic nerve sheath or sphenoid bone margin are exceptionally rare ectopic lesions. Because of their non-specific clinical presentation with unilateral progressive proptosis and visual decline, they are frequently misdiagnosed as cavernous hemangiomas or optic nerve gliomas. This study presents the surgical orbitotomy approach and complete vision preservation in an ectopic intraconal meningioma.
Keywords: Orbital meningioma Ectopic meningioma Intraconal mass Vision preservation Orbitotomy

Introduction & Background

Meningiomas in the orbit typically originate from arachnoid cap cells of the optic nerve sheath (OONM) or represent secondary extensions from sphenoid ridge cranial meningiomas. True ectopic intraconal orbital meningiomas arise from displaced embryological arachnoid rests within the orbital soft tissue.

Clinical Case Presentation & Diagnosis

A 38-year-old female presented with progressive painless proptosis and diminishing visual acuity (6/18) in the right eye over 14 months. Orbital MRI demonstrated a well-delineated, homogenously enhancing 2.2 cm intraconal retrobulbar mass displacing the optic nerve medially and inferiorly without direct nerve infiltration.

Surgical Technique & Management

A lateral orbitotomy approach with microsurgical bone osteotomy was utilized. Under high operative magnification, the orbital periorbita was opened and the intraconal space was accessed between the lateral rectus and superior rectus muscles. The tumor was separated cleanly from orbital fat and the adjacent ophthalmic artery branches and excised completely.

Discussion & Literature Context

Preservation of central retinal blood supply and the delicate ciliary ganglion is critical during intraconal dissection. Histopathology confirmed meningothelial meningioma (WHO Grade I). The patient experienced complete resolution of proptosis with visual acuity improving to 6/6 at 6-month follow-up.

Conclusion

Ectopic intraconal meningiomas can be cured with complete vision retention through meticulous micro-orbitotomy dissection.

How to Cite This Research

A. K. Sharma, C. S. Gandhoke, S. Misra, A. Ravi, R. K. Gupta, Dr. Surendra K. Gupta (2021). "Ectopic intraconal orbital meningioma–A rare case report". Surgical Neurology International, Volume 12, Article 305.

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